An autopsy case of congenital hepatic fibrosis and medullary sponge kidney with secondary gout.
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چکیده
منابع مشابه
A Case of Congenital Hepatic Fibrosis Associated With Medullary Sponge Kidney-Radiologic and Pathologic Features
Congenital hepatic fibrosis is an exceedingly rare disease in China, where only very few cases with sufficient evidences and clinical data have been reported up to now. Here we reported a young patient, onset of hematemesis and melena, who had striking portal hypertension but without liver function damage. Computer tomography scans showed hepatosplenomegaly, intra-hepatic bile ducts dilation, t...
متن کاملCongenital hepatic fibrosis in an aborted calf
An aborted female Holstein foetus with marked generalized anasarca was referred to the Excellence Centre for Ruminant Abortion and Neonatal Mortality, Ferdowsi University of Mashhad. On postmortem examination, red-tinged ascites, pale and firm liver with extreme irregularity and numerous round to oval slightly raised foci on the capsular surface were seen. Histological examination revealed wide...
متن کاملCongenital Hepatic Fibrosis: An Uncommon Cause of Chronic Renal Failure
Congenital Hepatic Fibrosis (CHF) is a rare disease that affects both the liver and kidneys. Congenital hepatic fibrosis (CHF) is an autosomal recessive inherited malformation defined pathologically by a variable degree of periportal fibrosis and irregularly shaped proliferating bile ducts. Affected individuals also have impaired renal function, usually caused, in children and teenagers, by an...
متن کامل[A case of medullary sponge disease associated with horseshoe kidney].
A 60-year-old man visited our hospital with complaints of micturition pain and interruption of urinary stream. X-ray examinations were performed, showing no bladder and urethral stone. However, KUB revealed bilateral multiple renal stones. Excretory urography showed a horseshoe kidney and a concentration of the contrast medium in the ectatic tubules at the pyramidal apices. Calculi were also lo...
متن کاملMedullary Sponge Kidney
Medullary sponge kidney (MSK) is a congenital disorder that can affect one or both kidneys, or only part of one kidney. There are ectatic and cystic changes of the medullary and papillary collecting ducts. This cystic dilatation of tubules may have an effect on urinary flow. Cysts can be 1-7 mm in diameter. Cyst formation is commonly associated with the development of small calculi within the c...
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ژورنال
عنوان ژورنال: Nihon Naika Gakkai Zasshi
سال: 1987
ISSN: 0021-5384,1883-2083
DOI: 10.2169/naika.76.1098